Parry–Romberg Syndrome in A Young Male

Abstract

Parry–Romberg syndrome is a condition in which there is slow and progressive shrinkage of the tissues and sometimes bones of one or occasionally both sides of the face. We report a rare case of Parry-Romberg syndrome with trigeminal neuralgia in a 27 year old male with complaints of right sided headache (on and off) and right sided facial pain, which was intermittent and progressive in nature since past 6 months. On physical examination, signs of right sided hemi atrophy and atrophied right side of lip and tongue was evident, whereas, left side appeared normal. Examination of the face revealed no sensory or motor deficits on both sides. On local examination, facial measurements showed hemi facial atrophy of the right side. Ultrasound abdomen, X-ray chest and X-ray skull revealed no abnormalities. Computerized Tomogram brain (CT) appeared normal with no midline shift, and no evidence of cerebral edema or cerebral atrophy. However, nerve conduction study showed features suggestive of trigeminal neuralgia of right side. Supportive and conservative management showed satisfactory response. On neurologist’s opinion, Carbamezipine 200 mg three times a day was started to which he showed remarkable improvement. We concluded that progressive hemi-facial atrophy is disease of unknown aetiology and rare pathology. Parry-Romberg syndrome is a self-limiting condition and there is no cure. Patients, who manifest atrophy in early ages, have a better outcome. Affected patients should have multi-disciplinary attendance of physicians, dentists, and psychologists. Recovery period for overall prognosis of Parry-Romberg syndrome is unpredictable.

Keywords: Parry–Romberg syndrome, progressive hemi-facial atrophy, trigeminal neuralgia, oral and maxillofacial surgery

Cite this Article:

Tanvi Vijay, Abhishek Kumar Singh, Sushmita Mitra, et al. Parry–Romberg Syndrome in a Young Male. Research and Reviews: Journal of Dentistry (RRJoD). 2015; 6(1): 14–17p.