Orbital Cellular Angiofibroma: One of the Rarest Tumor in Pandora’s Box

Abstract

Orbital cellular angiofibroma is one of the rarest benign mesenchymal tumors and only two cases have been reported. It typically originates from the lower reproductive tract and does not show a gender or race preference. Total surgical resection is the suggested modality of treatment. Diagnosing tumors in rare anatomical locations can pose considerable challenges, especially when they share common histopathological characteristics with more common tumors. In such cases, achieving an accurate diagnosis often demands a meticulous approach involving comprehensive histopathological analysis and immunohistochemistry. Our reported case involves a young female, underscoring the significance of maintaining a high index of suspicion when encountering unusual clinical presentations. To effectively diagnose a rare tumor in an atypical location, it is imperative to conduct thorough clinical assessments, utilize advanced radiological imaging techniques, and employ precise histopathological analyses. This multidisciplinary approach is essential for achieving a precise diagnosis, enabling the development of tailored treatment strategies, and ultimately improving patient outcomes.